myeloproliferative disease.

Abstract

Budd-Chiari syndrome (BCS) is the liver disease resulting from hepatic venous outflow obstruction comprising a triad of abdominal discomfort, hepatomegaly and ascites. Advances in the management of this disorder over the last three decades have dramatically improved survival.

We present a review of the management of BCS followed by a case which illustrates some key points in the diagnosis and treatment of this condition.